小耳畸形为先天性耳廓发育畸形,畸形轻重程度可有很大不同。最重度畸形表现为无耳,最轻者呈现近似耳廓的形态,但明显小于正常。这两种情况都较少见。绝大多数小耳畸形,系由皱缩而无耳廓形态的小块软骨团,和外形较正常但向前上方移位的耳垂所构成。无外耳道和鼓室、且听骨发育不良,有听力障碍。先天性小耳并非罕见。据统计其发生率约为1:20000。单双侧之比约为8:1。因耳廓位于明显部位,其形态失常对患儿心理发育极有影响。治疗主要有手术修复,施行全耳廓再造术。疗效尚好。...
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