肉芽肿性血管炎(GranulomatosiswithPolyangiitis,GPA),既往称为韦格纳肉芽肿(Wegenersgranulomatosis,WG)。是一种坏死性肉芽肿性血管炎,属自身免疫性疾病。该病病变累及小动脉、静脉及毛细血管,偶尔累及大动脉,其病理以血管壁的炎症为特征,主要侵犯上、下呼吸道和肾脏,通常以鼻黏膜和肺组织的局灶性肉芽肿性炎症为开始,继而进展为血管的弥漫性坏死性肉芽肿性炎症。...
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