肺血管炎最常见于原发性系统性血管炎病、胶原性血管炎病等。本病的基本病变是血管炎。即伴有肺实质的破坏(即坏死的血管壁炎细胞浸润)及肉芽肿性炎症。其中大部分疾病的原发性始动性病变是血管炎。肺血管炎的全身症状包括:发热、乏力、关节痛和皮损等,尤其以系统性血管炎和结缔组织病患者居多。...
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